Generic placeholder image

Current Cardiology Reviews

Author(s): Munish Dev*, Madhurima Sharma and Naresh Rana

DOI: 10.2174/1573403X15666190513105231

DownloadDownload PDF Flyer Cite As
Large Unrepaired Aortopulmonary Window Presenting in Adulthood

Page: [73 - 76] Pages: 4

  • * (Excluding Mailing and Handling)

Abstract

Background: Aortopulmonary window is an uncommon congenital heart disease, with untreated cases not surviving beyond childhood. However, very rarely it can present in adult patients with features of pulmonary hypertension. Clinically these patients cannot be differentiated from other more common conditions with left to right shunt. Transthoracic echocardiography if performed meticulously, can depict the defect in aortopulmonary septum.

Results: We report a case of large unrepaired aortopulmonary window in a 23 years old patient, diagnosed on transthoracic echocardiography.

Keywords: Echocardiography, congenital heart disease, pulmonary artery hypertension, computed tomography, aortopulmonary window, transthoracic echocardiography.

Graphical Abstract

[1]
Richardson JV, Doty DB, Rossi NP, Ehrenhaft JL. The spectrum of anomalies of aortopulmonary septation. J Thorac Cardiovasc Surg 1979; 78(1): 21-7.
[PMID: 449383]
[2]
Aggarwal SK, Mishra J, Sai V, Iyer VR, Panicker BK. Aortopulmonary window in adults: Diagnosis and treatment of late-presenting patients. Congenit Heart Dis 2008; 3(5): 341-6.
[http://dx.doi.org/10.1111/j.1747-0803.2008.00210.x] [PMID: 18837813]
[3]
Ganju NK, Kandoria A. Aortopulmonary window: A rare cardiac anomaly presenting in adolescent age group. Heart India 2015; 3: 87.
[http://dx.doi.org/10.4103/2321-449X.157284]
[4]
Shewale R, Sharma A, Mishra H. A large aortopulmonary window with a ventricular septal defect: A rare combination presenting at the age of 16. Cardiology and angiology. Int J 2018; 7: 1-5.
[5]
Backer CL. Aortopulmonary window and aortic origin of a pulmonary artery. In: Pediatric Cardiac Surgery. 2003.
[6]
Mori K, Ando M, Takao A, Ishikawa S, Imai Y. Distal type of aortopulmonary window. Report of 4 cases. Br Heart J 1978; 40(6): 681-9.
[http://dx.doi.org/10.1136/hrt.40.6.681] [PMID: 656242]
[7]
Balaji S, Burch M, Sullivan ID. Accuracy of cross-sectional echocardiography in diagnosis of aortopulmonary window. Am J Cardiol 1991; 67(7): 650-3.
[http://dx.doi.org/10.1016/0002-9149(91)90910-D] [PMID: 2000804]
[8]
Sridhar PG, Kalyanpur A, Suresh PV, Sharma R, Maheshwari S, Hrudayalaya N. Helical CT evaluation of aortopulmonary window. Indian J Radiol Imaging 2006; 16: 847.
[http://dx.doi.org/10.4103/0971-3026.32364]
[9]
Garver KA, Hernandez RJ, Vermilion RP, Martin Goble M. Images in cardiovascular medicine. Correlative imaging of aortopulmonary window: demonstration with echocardiography, angiography, and MRI. Circulation 1997; 96(3): 1036-7.
[http://dx.doi.org/10.1161/01.CIR.96.3.1036] [PMID: 9264517]
[10]
Trehan V, Nigam A, Tyagi S. Percutaneous closure of nonrestrictive aortopulmonary window in three infants. Catheter Cardiovasc Interv 2008; 71(3): 405-11.
[http://dx.doi.org/10.1002/ccd.21366] [PMID: 18288731]
[11]
Perloff JK, Rosove MH, Child JS, Wright GB. Adults with cyanotic congenital heart disease: hematologic management. Ann Intern Med 1988; 109(5): 406-13.
[http://dx.doi.org/10.7326/0003-4819-109-5-406] [PMID: 3044212]
[12]
Stout KK, Daniels CJ. Aboulhosn et al. 2018 AHA/ACC guideline for the management of adults with congenital heart disease: A report of the American College of Cardiology/American Heart Association Task Force on Clinical Practice Guidelines. Circulation 2018.CIR-0000000000000603