Current Treatment Options for the Failing Fontan Circulation

Bart   W.   Driesen; Michiel      Voskuil; Heynric   B.   Grotenhuis
Abstract

The Fontan operation was introduced in 1968. For congenital malformations, where biventricular repair is unsuitable, the Fontan procedure has provided a long-term palliation strategy with improved outcomes compared to the initially developed procedures. Despite these improvements, several complications merely due to a failing Fontan circulation, including myocardial dysfunction, arrhythmias, increased pulmonary vascular resistance, protein-losing enteropathy, hepatic dysfunction, plastic bronchitis, and thrombo-embolism, may occur, thereby limiting the life-expectancy in this patient cohort. This review provides an overview of the most common complications of Fontan circulation and the currently available treatment options.
Keywords: Pediatrics, heart defects, congenital, fontan, complications, treatment.
Graphical Abstract

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Cite As
Current Cardiology Reviews

Current Treatment Options for the Failing Fontan Circulation

Abstract

Graphical Abstract
